Hepatopulmonary syndrome: diagnostics, pathogenesis, clinical symptomatology and methods of treatment
Abstract
The aim of review. To analyze literature data on definition of hepatopulmonary syndrome (HPS), its diagnostics, pathogenesis, features of clinical presentation and treatment options.
Recent literature data. HPS is complication of liver diseases, leading to disorders of perfusion in lungs and decrease of blood oxygenation. Diagnostics of this syndrome requires triad of signs: chronic liver disease, dilation of intrapulmonic vessels, decrease of arterial blood oxygenation. For the present time the concepts of causes and pathogenesis of pulmonary vasodilatation and disorders of blood gases composition at HPS are still inconsistent.
Conclusion. Up to now the definite algorithm of diagnostics and management of patients with HPS is not developed.
About the Authors
V. T. IvashkinRussian Federation
M. A. Morozova
Russian Federation
M. V. Maevskaya
Russian Federation
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Review
For citations:
Ivashkin V.T., Morozova M.A., Maevskaya M.V. Hepatopulmonary syndrome: diagnostics, pathogenesis, clinical symptomatology and methods of treatment. Russian Journal of Gastroenterology, Hepatology, Coloproctology. 2008;18(2):12-17. (In Russ.)
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